bloodjourГематология и трансфузиологияRussian journal of hematology and transfusiology0234-57302411-3042ООО Издательский дом «Практика»10.35754/0234-5730-2022-67-1-131-138bloodjour-342Research ArticleКЛИНИЧЕСКИЕ НАБЛЮДЕНИЯCASE REPORTSХирургическое лечение гемофилической артропатии подтаранного сустава у больного тяжелой формой гемофилии ВSurgical treatment of hemophilic arthropathy of subtalar joint in a patient with severe hemophilia Bhttps://orcid.org/0000-0003-3198-9985ПашковаЕ. А.PashkovaE. A.

Пашкова Екатерина Анатольевна, аспирант, врач травматолог-ортопед 

195427, Санкт-Петербург

Ekaterina A. Pashkova, Postgraduate student, Orthopedic Surgeon 

195427, Saint Petersburg

caterinapashkova@yandex.ruhttps://orcid.org/0000-0002-9948-9015СорокинЕ. П.SorokinE. P.

Сорокин Евгений Петрович, кандидат медицинских наук, научный сотрудник 

195427, Санкт-Петербург

Evgenii P. Sorokin, Cand. Sci. (Med.), Orthopedic Surgeon, Researcher 

195427, Saint Petersburg

sorokinortoped@gmail.comhttps://orcid.org/0000-0001-6284-7133КасимоваА. Р.KasimovaA. R.

Касимова Алина Рашидовна, клинический фармаколог отделения клинической фармакологии; ассистент кафедры клинической фармакологии и доказательной медицины 

195427, Санкт-Петербург; 197022, Санкт-Петербург

Alina R. Kasimova, Clinical Pharmacologist; Teaching Assistant at the Department of Clinical Pharmacology and Evidence-Based Medicine 

195427, Saint Petersburg;197022, Saint Petersburg

kasi-alina@yandex.ruФГБУ «Национальный медицинский исследовательский центр травматологии и ортопедии им. Р.Р. Вредена» Министерства здравоохранения Российской ФедерацииРоссияRussian Scientific Research Institute of Traumatology and Orthopedics named after R.R. VredenRussian FederationФГБУ «Национальный медицинский исследовательский центр травматологии и ортопедии им. Р.Р. Вредена» Министерства здравоохранения Российской Федерации; ФГБОУ ВО «Первый Санкт-Петербургский государственный медицинский университет им. акад. И.П. Павлова» Министерства здравоохранения Российской ФедерацииРоссияRussian Scientific Research Institute of Traumatology and Orthopedics named after R.R. Vreden; Academician I.P. Pavlov First St. Petersburg State Medical University of the Ministry of Healthcare of Russian FederationRussian Federation202213042022671131138Copyright © Пашкова Е.А., Сорокин Е.П., Касимова А.Р., 20222022Пашкова Е.А., Сорокин Е.П., Касимова А.Р.Pashkova E.A., Sorokin E.P., Kasimova A.R.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://www.htjournal.ru/jour/article/view/342Введение

Введение. Гемофилическая артропатия и развивающийся на ее фоне остеоартрит крупных суставов стопы часто требуют хирургического лечения. Течение гемофилии и  необходимость коррекции факторов свертывания крови затрудняют ведение больного, а недостаточная осведомленность оперирующего хирурга может послужить причиной для отказа от вмешательства.

Цель  — представить клиническое наблюдение лечения гемофилической артропатии подтаранного сустава у больного гемофилией В, которому была выполнена операция артродезирования.

Основные сведения

Основные сведения. Наблюдение демонстрирует сложность периоперационного ведения и  необходимость подбора и коррекции индивидуальной заместительной терапии. Клинический случай может представлять интерес для врачей травматологов, ортопедов, а также клинических фармакологов, работающих на базе хирургических стационаров.

Introduction

Introduction. Hemophilic arthropathy and the subsequent development of osteoarthritis in the large foot joints often require surgical intervention. At the same time, the course of hemophilia and the need to correct blood clotting factors make it diffi cult to manage the patient. The lack of awareness of the operating surgeon can serve as a reason for refusing the operation.

Aim — to present a clinical case of hemophilic arthropathy of the subtalar joint in a patient with hemophilia B who underwent fusion.

Main findings

Main findings. The observation demonstrates the complexity of perioperative management and the need for the selection and correction of individual factor replacement therapy. A clinical case may be of interest to trauma surgeons, orthopedists, as well as clinical pharmacologists working in surgical hospitals.

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The authors declare that there are no conflicts of interest present.