SECONDARY IMMUNE THROMBOCYTOPENIA IN THE PRIMARY IMMUNODEFICIENCY DISORDER IN ADULT HEMATOLOGICAL PRACTICE
A. L. Melikyan,
E. K. Egorova,
M. V. Kalinina,
E. I. Pustovaya,
T. I. Kolosheynova,
E. A. Gilyazitdinova,
I. N. Subortseva https://doi.org/10.18821/0234-5730-2017-62-3-159-163
Abstract
Thrombocytopenia is a symptom of a wide range of hematological and non-hematological diseases, requiring extensive diagnostic search. Rapid detection of the main cause of thrombocytopenia affects the prognosis and therapeutic tactics in a number of patients with hematological diseases. One of the reasons for the development of secondary thrombocytopenia are primary immunodeficiency disorders (PID), whose debut is possible at the age of over 18 years. Diagnosis of this pathology is difficult, due to the low alertness of primary care physicians about the presence of favorably occurring primary immunodeficiencies, the first manifestation of which can be the immune thrombocytopenia revealed in an adult. This article is devoted to the report of the clinical cases of newly diagnosed PID in adulthood, debuting from autoimmune complications.
About the Authors
A. L. Melikyan
National Research Center for Hematology
Russian Federation
Russian Federation
Moscow, 125167
Melikyan Anait Levonovna, MD, PhD, DSc., Head Department of standardization of methods therapy
ResearcherID: M-7116-2014
E. K. Egorova
National Research Center for Hematology, Moscow
Russian Federation
ResearcherID: G-3839-2016
Russian Federation
ResearcherID: G-3839-2016
M. V. Kalinina
National Research Center for Hematology, Moscow
Russian Federation
Russian Federation
E. I. Pustovaya
National Research Center for Hematology, Moscow
Russian Federation
Russian Federation
T. I. Kolosheynova
National Research Center for Hematology, Moscow
Russian Federation
Russian Federation
E. A. Gilyazitdinova
National Research Center for Hematology, Moscow
Russian Federation
Russian Federation
I. N. Subortseva
National Research Center for Hematology, Moscow
Russian Federation
ResearcherID: M-7101-2014
Russian Federation
ResearcherID: M-7101-2014
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For citations:
Melikyan A.L., Egorova E.K., Kalinina M.V., Pustovaya E.I., Kolosheynova T.I., Gilyazitdinova E.A., Subortseva I.N. SECONDARY IMMUNE THROMBOCYTOPENIA IN THE PRIMARY IMMUNODEFICIENCY DISORDER IN ADULT HEMATOLOGICAL PRACTICE. Russian journal of hematology and transfusiology. 2017;62(3):159-163. (In Russ.) https://doi.org/10.18821/0234-5730-2017-62-3-159-163
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