CASE OF SURGICAL TREATMENT OF MULTI-LOCALIZED PSEUDOTUMORS IN PATIENT WITH INHIBITOR HAEMOPHILIA A
V. Yu. Zorenko,
T. Yu. Polyanskaya,
N. V. Sadykova,
G. M. Galstyan,
E. E. Karpov,
M. S. Sampiev,
G. V. Mishin,
A. V. Golobokov,
I. E. Kostina,
D. A. Kudlaj https://doi.org/10.25837/HAT.2019.15.30.005
Abstract
Pseudotumors are rare complication in hemophilia patients, occurring in 1—2% of cases. The triggering mechanism of pseudotumor development is hematoma, which can transform into pseudotumor when the treatment is differed or not full. The most severe complication of pseudotumor are destruction of underlying tissues, infection and spontaneous dissection of the pseudotumor and the development of uncontrolled bleeding. Often pseudotumors are confused with malignant neoplasms, which leads to errors in the algorithms of examination and treatment of patients with hemophilia and pseudotumors. Therefore, the clinical case of treatment of giant pseudotumors of multiple localization at patient with an inhibitory form of hemophilia seems to be of interest.
About the Authors
V. Yu. Zorenko
National Research Center for Hematology
Russian Federation
Moscow
Russian Federation
Moscow
T. Yu. Polyanskaya
National Research Center for Hematology
Russian Federation
Moscow
Russian Federation
Moscow
N. V. Sadykova
National Research Center for Hematology
Russian Federation
Moscow
Russian Federation
Moscow
G. M. Galstyan
National Research Center for Hematology
Russian Federation
Moscow
Russian Federation
Moscow
E. E. Karpov
National Research Center for Hematology
Russian Federation
Moscow
Russian Federation
Moscow
M. S. Sampiev
National Research Center for Hematology
Russian Federation
Moscow
Russian Federation
Moscow
G. V. Mishin
National Research Center for Hematology
Russian Federation
Moscow
Russian Federation
Moscow
A. V. Golobokov
National Research Center for Hematology
Russian Federation
Moscow
Russian Federation
Moscow
I. E. Kostina
National Research Center for Hematology
Russian Federation
Moscow
Russian Federation
Moscow
D. A. Kudlaj
Institute for Advanced Studies of FMBA of Russia
Russian Federation
Moscow
Russian Federation
Moscow
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Review
For citations:
Zorenko V.Yu., Polyanskaya T.Yu., Sadykova N.V., Galstyan G.M., Karpov E.E., Sampiev M.S., Mishin G.V., Golobokov A.V., Kostina I.E., Kudlaj D.A. CASE OF SURGICAL TREATMENT OF MULTI-LOCALIZED PSEUDOTUMORS IN PATIENT WITH INHIBITOR HAEMOPHILIA A. Russian journal of hematology and transfusiology. 2018;63(3):258-265. (In Russ.) https://doi.org/10.25837/HAT.2019.15.30.005
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